Prune-Belly Syndrome. A case presentation

Authors

  • Oscar Portela Rodríguez
  • Bárbara Ojeda Pino
  • Amalay Luna
  • Susana Pino Muñoz
  • Iranaka Avello Benedico
  • Libbys Carrera Espinosa

Abstract

The Prune-Belly syndrome is a distinct entity of unknown etiology, consisting of a spectrum of congenital malformations able to lead the pregnancy to abortion, or post-natal complications usually urinary of varying degrees of morbidity / mortality, which will determine the outcome of the infant born with this condition. Although it is a clinical picture with a very low mortality, the consequences are different for health and quality of infants life. In this research a case of Prune-Belly that was born at 36 weeks gestation, who presented the classic findings of this rare syndrome is reported.

Downloads

Download data is not yet available.

Author Biographies

Oscar Portela Rodríguez

Especialista de 1er Grado en Neonatología. Máster en Atención Integral al Niño.

Bárbara Ojeda Pino

Médico.

Amalay Luna

Especialista de 1er Grado en Medicina General Integral. Especialista de 1er Grado en Neonatología.

Susana Pino Muñoz

Especialista de 2do Grado en Neonatología. Máster en Atención Integral al Niño.

Iranaka Avello Benedico

Especialista de 1er Grado en Medicina General Integral.

References

Bogart MM, Arnold HE, Greer KE. Prune-Belly syndrome in two children and review of the literature. Pediatr Dermatol. 2006; 23(4):342-5.

Evans MG, Poulsen RR, Fritz JE, Valenzuela SN. Alteraciones de las extremidades inferiores en el síndrome de Prune-Belly. Rev Chil Ultras. 2003; 6(4):130-4.

Bouzada M, Avelar JH, Souza LC de, Silva JMP. Trissomia do 21 e síndrome de Prune Belly: relato de caso. Rev Méd Minas Gerais. 2003; 13(1):56-9.

Malo G, Ferro A, Orjuela C. Manejo integral de los pacientes con síndrome de Prune-Belly. Urol Colombiana. 2000; 9(2):51-6.

Barriga J. Síndrome de Prune-Belly: comunicación de un caso clínico. Carta Med A.I.S. Boliv. 2002; 17(1):15-6.

Ramasamy R, Haviland M, Woodard JR, Barone JG. Patterns of inheritance in familial Prune Belly syndrome. Urology. 2005; 65(6):1227.

Weber S, Mir S, Schlingmann KP. Gene locus ambiguity in posterior urethral valves/prune-belly syndrome. Pediatr Nephrol. 2005; 20(8):036-42.

Heini PF, Locher S, Schede CP, Anderson S, Slongo T. Surgical treatment with the technique of Galveston-Luque of spine deformities associated with the Prune Belly syndrome. J Pediatr Orthop B. 2004; 13(4):231-7.

Salihu HM, Tchuinguem G, Aliyu MH, Kouam L. Prune Belly syndrome and associated malformations. A 13-year experience from a developing country. West Indian Med J. 2003; 52(4):281-4.

Strand WR. Initial management of complex pediatric disorders: prune belly syndrome, posterior urethral valves.Urol Clin North Am. 2004; 31(3):399-415.

Poucell-Hatton S, Huang M, Bannykh S, Benirshke K, Masliah E. Fetal obstructive uropathy: patterns of renal pathology. Pediatr Developm Pathol 2000; 3: 223-31.

Keating M, Duckett J. Síndrome de abdomen en ciruela pasa. En: Cirugía Pediátrica. México: Editorial Panamericana; 1995. p. 743-62.

Behrman R, Kliegman R, Nelson W, Vaughan V. Nelson. Tratado de Pediatría 14 ed. Madrid: Editorial Mc Graw Hill Interamericana; 1992.

Pagon RA, Smith DW, Shepard TH. Urethral obstruction malformation complex: a cause of abdominal muscle deficiency and the "Prunne-Belly". J Pediatr. 1979; 94: 900-6.

Godman RM, Gorlin RJ. Malformaciones en el lactante y el niño. Guía Ilustrada. Madrid: Salvat; 1986.

Krebs C. Defectos congénitos de la pared abdominal. En: Pediatría Meneghello: Buenos Aires: Editorial Médica Panamericana; 1997.

Mahony BS, Callen PW, Filly RA. Fetal urethral obstruction: US evaluation. Radiology. 1985; 157: 221.

Rumack CM, Wilson SR, Charboneau JW. Ecografía obstétrica y fetal. Madrid: Editorial Marbán Libros; 1999.

Glazer GM, Filly RA, Callen PW. The varied sonographic appearance of the urinary tract in the fetus and newbornwith urethral obstruction. Radiology. 1982; 144:563.

Sanders RC, Nussbaum AR, Solez K. Renal dysplasia: sonographic findings. Radiology. 1988; 167:623.

Published

2014-12-19

How to Cite

1.
Portela Rodríguez O, Ojeda Pino B, Luna A, Pino Muñoz S, Avello Benedico I, Carrera Espinosa L. Prune-Belly Syndrome. A case presentation. Mediciego [Internet]. 2014 Dec. 19 [cited 2024 Nov. 24];20(2). Available from: https://revmediciego.sld.cu/index.php/mediciego/article/view/139

Issue

Section

Case Report

Most read articles by the same author(s)

<< < 1 2