Retroperitoneal sarcoma. Case report
Keywords:
abdominal neoplasms, retroperitoneal neoplasms, sarcomaAbstract
Introduction: primary retroperitoneal tumors are solid or cystic, benign or malignant. They develop in the retroperitoneal space, from tissues (lymphatic, nervous, vascular, supporting muscle, connective and fibroareolar) independent of the organs and large vessels contained therein, such as the kidney, the adrenal glands and the retroperitoneal parts of the pancreas, colon, and duodenum. The most frequent are sarcomas in their different varieties, fundamentally liposarcoma and leiomyosarcoma. Both present as abdominal masses with a hard consistency and irregular surface, surrounded by a capsule that is rapidly overwhelmed by tumor growth. These tumors infiltrate the parietal peritoneum and the intra-abdominal viscera attached to it.
Objective: to present the case of a patient diagnosed with giant retroperitoneal sarcoma, successfully treated at "Hermanos Ameijeiras" Surgical Clinical Hospital.
Case presentation: 67-year-old male patient, with a clinical picture of volume increase towards the left hemiabdomen, associated with decay and weight loss. The biopsy of the tumor lesion reported the presence of a fusocellular sarcoma. He was initially treated with chemotherapy, and subsequently underwent surgery with removal of the tumor and splenectomy.
Conclusions: surgical intervention continues to be the therapeutic option of choice, and the management of these patients must be carried out in a timely manner. Due to the complexity and characteristics of the surgical intervention, a high learning curve and experience of the specialist is necessary.Downloads
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